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Telangiectasia macularis eruptiva perstans in Child
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Telangiectasia macularis eruptiva perstans in Child

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Contributors: Tyler Werbel, Susan Burgin MD
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Synopsis

Telangiectasia macularis eruptiva perstans (TMEP) is a form of cutaneous mastocytosis that results from mast cell accumulation in the skin. These pruritic lesions persist over time and can be found anywhere on the skin surface. Usually, the patient is asymptomatic from both a cutaneous and a systemic standpoint, but, rarely, there may be systemic involvement of gastrointestinal, musculoskeletal, or pulmonary systems, which has been shown to correlate with serum tryptase levels. TMEP almost exclusively affects adults, but it has been described in children. It follows a benign course, and treatment is symptomatic.

The 2016 World Health Organization (WHO) classification of mastocytosis does not mention TMEP as a separate form of cutaneous mastocytosis: it has been folded into the maculopapular cutaneous mastocytosis / urticaria pigmentosa category in this classification system.

Codes

ICD10CM:
Q82.2 – Mastocytosis

SNOMEDCT:
8214000 – Telangiectasia macularis eruptiva perstans

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Last Reviewed: 09/25/2018
Last Updated: 09/25/2018
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Telangiectasia macularis eruptiva perstans in Child
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Telangiectasia macularis eruptiva perstans : Darier's sign positive, Erythema, Primarily truncal, Telangiectasia, Widespread, Pruritus
Clinical image of Telangiectasia macularis eruptiva perstans
Numerous telangiectatic macules and patches on the thigh with 3 small wheals (positive Darier sign).
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