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Tolosa-Hunt syndrome
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Tolosa-Hunt syndrome

Contributors: Andrea Wasilewski MD, Richard L. Barbano MD, PhD
Other Resources UpToDate PubMed

Synopsis

Tolosa-Hunt syndrome is a rare, idiopathic granulomatous inflammation of the cavernous sinus, superior orbital fissure, or orbit that leads to unilateral headache and orbital pain with diplopia and ipsilateral paresis of cranial nerves III, IV, VI, and/or the superior branches of V. Occasionally, vision can be affected. Patients may present at any age. This condition is typically unilateral but can be bilateral in 5% of cases.

Symptoms are very responsive to glucocorticoids but tend to relapse and remit if left untreated. The syndrome can resolve spontaneously or result in permanent neurologic damage.

Codes

ICD10CM:
H49.40 – Progressive external opthalmoplegia, unspecified eye

SNOMEDCT:
95794005 – Tolosa-Hunt syndrome

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Differential Diagnosis & Pitfalls

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Therapy

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References

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Last Reviewed:07/26/2018
Last Updated:07/26/2018
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Tolosa-Hunt syndrome
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Tolosa-Hunt syndrome : Fatigue, Headache, Diplopia, Eyelid ptosis, Proptosis, Unilateral retroorbital pain
Copyright © 2021 VisualDx®. All rights reserved.