Tufted angioma - Skin
Tufted angioma typically presents at birth (50% of cases) or within the first year of life as a violaceous plaque or nodule that may be painful. Rarely, it presents during childhood or early adulthood. There may be a slight male predominance.
After an initial period of growth, the tumor stabilizes and usually persists; in some patients it may spontaneously, partially, or completely regress.
Tufted angiomas may be associated with a coagulopathy or with Kasabach-Merritt phenomenon (KMP), a potentially life-threatening condition characterized by an enlarging vascular lesion, profound thrombocytopenia, consumptive coagulopathy, and often a microangiopathic hemolytic anemia.
For more information, see OMIM.
D18.01 – Hemangioma of skin and subcutaneous tissue
254786000 – Tufted angioma of skin
- Infantile hemangioma – asymptomatic and soft, rapidly grows before a slow involution, no associated coagulopathy
- Vascular malformation (eg, arteriovenous malformations, port-wine stain, Klippel-Trenaunay syndrome, acroangiodermatitis, lumbosacral infantile hemangioma, angioma serpiginosum, lymphangioma circumscriptum, MCAP)
- Infantile myofibromatosis
- Congenital dermatofibrosarcoma protuberans
- Kaposiform hemangioendothelioma