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Unilateral nevoid telangiectasias in Adult
Other Resources UpToDate PubMed

Unilateral nevoid telangiectasias in Adult

Contributors: Chris G. Adigun MD, David Dasher MD
Other Resources UpToDate PubMed

Synopsis

Unilateral nevoid telangiectasia (UNT), also known as unilateral dermatomal superficial telangiectasia, is a cutaneous condition characterized by telangiectasias present in a dermatomal or Blaschkoid distribution. UNT most commonly involves the C3-C4 or trigeminal dermatomal regions, and it may be congenital or acquired. The congenital form is less common and has a male predominance, whereas the acquired form is more common and has a female predominance. The condition is asymptomatic.

Acquired UNT typically occurs in conjunction with physiologic states of elevated estrogen levels, such as hormonal therapy, puberty, and pregnancy in women, and adrenarche in men. This condition has also been reported to develop in pathologic states of elevated estrogen, such as chronic hepatic disease and alcohol use disorder. However, there are reports of acquired UNT occurring in both children and adults in the setting of normal serum estrogen levels and normal liver function studies.

The etiology of UNT is unknown; the current theory is that UNT occurs in a circumstance of relative estrogen excess. This relative estrogen excess subsequently unmasks a localized increase in estrogen receptors caused by chromosomal mosaicism. Other speculated mechanisms for the development of UNT include neural alterations, hemodynamic disturbances, abnormalities in perivascular connective tissue, and angiogenic factors.

Codes

ICD10CM:
I78.8 – Other diseases of capillaries

SNOMEDCT:
767127000 – Unilateral nevoid telangiectasia

Look For

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Diagnostic Pearls

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Differential Diagnosis & Pitfalls

Disorders of primary telangiectasia:
Disorders of secondary telangiectasia:
Spider angiomas associated with pregnancy, alcohol use disorder, and liver disease (cirrhosis, hepatitis)

Best Tests

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Management Pearls

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Therapy

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Drug Reaction Data

Below is a list of drugs with literature evidence indicating an adverse association with this diagnosis. The list is continually updated through ongoing research and new medication approvals. Click on Citations to sort by number of citations or click on Medication to sort the medications alphabetically.

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References

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Last Updated:06/08/2018
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Unilateral nevoid telangiectasias in Adult
Unilateral nevoid telangiectasias : Linear configuration, Telangiectasia, Unilateral distribution, Blanching macule
Clinical image of Unilateral nevoid telangiectasias
Close-up of numerous red, telangiectatic macules and papules with surrounding haloes.
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