Extramammary Paget disease
The condition is most often seen in elderly White women, but males are more likely to be diagnosed with this condition in Japan.
Clinically, lesions most commonly appear on the vulva in women and in the perianal area in men. Lesions are often banal in appearance and similar to the lesions of eczematous dermatoses, leading to delays in diagnosis. Symptoms may be minimal to none; sometimes, there is itch, pain, or burning. Presentation is typically of a red, sharply demarcated plaque that expands slowly. Areas within the plaque are marked by erosions and white scale, leading to the appearance of "strawberries and cream." EMPD is thought to invade and metastasize via lymphatics.
C44.99 – Other specified malignant neoplasm of skin, unspecified
71447003 – Paget's disease, extramammary (except Paget's disease of bone)
Differential Diagnosis & Pitfalls