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Optic nerve sheath meningioma
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Optic nerve sheath meningioma

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Contributors: Andrea Wasilewski MD, Richard L. Barbano MD, PhD
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Synopsis

Optic nerve sheath meningiomas (ONSM) are rare, slow-growing, benign tumors of the meninges surrounding the optic nerve. These tumors are classically found in adults after the 3rd decade of life, are rare in children, and occur more commonly in women than in men (3:2 ratio). Most patients will present with progressive monocular vision loss. Optic atrophy may be seen on examination. Patients with ONSM are frequently misdiagnosed with optic neuritis. Risk factors include prior radiation therapy exposure for central nervous system malignancies, incidental radiation exposure, and genetic conditions such as neurofibromatosis type 2 and schwannomatosis.

Treatment is often complicated and limited by the location of the tumor and can result in significant complications such as visual impairment and blindness. Morbidity from ONSM is low but the prognosis for visual recovery is variable, with many patients losing vision in the affected eye.

Codes

ICD10CM:
D33.3 – Benign neoplasm of cranial nerves

SNOMEDCT:
254978007 – Meningioma of optic nerve sheath

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Last Reviewed: 06/17/2019
Last Updated: 06/19/2019
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Optic nerve sheath meningioma
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Optic nerve sheath meningioma
Copyright © 2019 VisualDx®. All rights reserved.