Telangiectasia macularis eruptiva perstans in Adult
Alerts and Notices
Synopsis

The 2016 World Health Organization (WHO) classification of mastocytosis does not mention TMEP as a separate form of cutaneous mastocytosis: it has been folded into the maculopapular cutaneous mastocytosis / urticaria pigmentosa category in this classification system.
Codes
ICD10CM:Q82.2 – Mastocytosis
SNOMEDCT:
8214000 – Telangiectasia macularis eruptiva perstans
Look For
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Diagnostic Pearls
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Differential Diagnosis & Pitfalls
- Urticaria pigmentosa
- Nevus telangiectaticus (eg, port-wine stain)
- Glomus tumors
- CREST syndrome
- Fabry disease
- Spider telangiectasia secondary to underlying liver disease
- Freckles
- Nevi
- Poikiloderma vasculare atrophicans
- Poikiloderma of Civatte – typically seen in the neck region
- Rosacea – typically seen on the face
- Generalized essential telangiectasias
Best Tests
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Management Pearls
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Therapy
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References
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Last Reviewed:09/24/2018
Last Updated:12/16/2019
Last Updated:12/16/2019