PR has been classified into two distinct subtypes.
Type 1 occurs predominantly in elderly patients of Asian and African descent and is frequently associated with significant systemic illness such as infection or malignancy, particularly hepatocellular carcinoma or gastric cancer. Lesions are typically hyperpigmented and generally fewer than 40 are present.
Type 2 occurs primarily in patients of Northern European descent younger than 40 years. It has a strong hereditary predisposition. There is no association with systemic illness or malignancy. It is believed by many to exist along a spectrum of congenital ichthyoses. Lesions are typically hypopigmented and more numerous.
L44.8 – Other specified papulosquamous disorders
238639005 – Pityriasis rotunda
Differential Diagnosis & Pitfalls
- Congenital (eg, , ) and – Similar histopathologic findings.
- – Usually annular and can be confirmed by finding fungal hyphae on potassium hydroxide (KOH) preparation.
- – May present similarly but can be confirmed by finding fungal forms ("spaghetti and meatballs") on KOH preparation.
- – Will show evidence of bacteria on gram stain as well as coral red on Wood's lamp exam.